CASE: Prior to the emergence of bone marrow transplantation as a treatment for Hurler syndrome, most individuals with this syndrome did not survive into their teenage years. We describe a twenty-three-year-old patient with Hurler syndrome who had been treated with bone marrow transplantation; we focus on the presentation and treatment of the associated carpal tunnel syndrome and trigger digits. After initial trigger digit release and revision bilateral carpal tunnel release with a tenosynovectomy, he maintained symptom-free hand function.
CONCLUSION: Surgical treatment of median nerve compression and trigger digits due to Hurler syndrome is effective in the long term.